Diagnosing Cardiac Amyloidosis: From Heart Failure to Electrical Storm

Treatment of End Stage Heart Failure Related to Cardiac Amyloidosis

Amyloidosis is a disease characterized by deposition of extracellular proteinaceous mate‐ rial known as amyloid in tissues. Amyloidoses are classified according to the protein composition and the clinical characteristics of the disease [1]. Amyloid protein can accu‐ mulate at various speeds in multiple organ systems and the disease can have localized or systemic manifestations depending on orga...

Transthyretin cardiac amyloidosis: an under-diagnosed cause of heart failure

INTRODUCTION Cardiac amyloidosis is the most common cause of infiltrative cardiomyopathy and is associated with a poor prognosis. Transthyretin cardiac amyloidosis, particularly the type caused by the mutation that replaces the amino acid valine with the amino acid isoleucine at position 122 (Val122Ile), is most common among African- Americans above 65 years of age. Evidence suggests that this ...

Senile cardiac amyloidosis: an undervalued cause of heart failure.

Electrical storm secondary to acute myocardial infarction and heart failure treated with left stellate ganglion block.

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Obstructive intramural coronary amyloidosis: a distinct phenotype of cardiac amyloidosis that can cause acute heart failure.

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